Musculoskeletal evaluation in severe haemophilia A patients from Latin America


Por: Ozelo M.C., Villaça P.R., Pérez-Bianco R., Candela M., Garcia-Chavez J., Moreno-Rodriguez B., Rodrigues M.B., Rodriguez-Grecco I., Solano M.H., Chumpitaz G., Morales-Gana M.M., Ruiz-Sáez A.

Publicada: 1 ene 2014
Resumen:
There is a paucity of literature on haemophilia treatment in Latin American countries, a region characterized by rapidly improving systems of care, but with substantial disparities in treatment between countries. The aim of this study was to evaluate the musculoskeletal status of haemophilia patients from Latin America and to examine the relationship between musculoskeletal status and treatment practices across countries. The Committee of Latin America on the Therapeutics of Inhibitor Groups conducted a survey of its member country representatives on key aspects of haemophilia treatment in 10 countries. Musculoskeletal status of patients was obtained during routine comprehensive evaluations between March 2009 and March 2011. Eligible patients had severe haemophilia A (factor VIII <1%) without inhibitors (<0.6 BU mL-1) and were =5 years of age. Musculoskeletal status was compared between three groups of countries, based primarily on differences in the availability of long-term prophylaxis. Overall, 143 patients (5-66 years of age) were enrolled from nine countries. In countries where long-term prophylaxis had been available for at least 10 years (Group A), patients aged 5-10 years had significantly better mean World Federation of Hemophilia clinical scores, fewer target joints and fewer affected joints than patients from countries where long-term prophylaxis has been available for about 5 years (Group B) or was not available (Group C). In Latin America, the musculoskeletal status of patients with severe haemophilia without inhibitors has improved significantly in association with the provision of long-term prophylaxis. As more countries in Latin America institute this practice, further improvements are anticipated. © 2013 The Authors.

Filiaciones:
Ozelo M.C.:
 Unidade de Hemofilia IHTC 'Claudio L. P. Correa', Instituto Nacional de Tecnologia do Sangue, Hemocentro UNICAMP, University of Campinas, Campinas, Brazil

Villaça P.R.:
 Centro de Hemofilia, São Paulo, Brazil

 Hospital das Clinicas da Universidade de São Paulo (USP), São Paulo, Brazil

Pérez-Bianco R.:
 Instituto de Investigaciones Hematologicas 'Mariano Castex', Academia Nacional de Medicina, Buenos Aires, Argentina

Candela M.:
 Instituto de Investigaciones Hematologicas 'Mariano Castex', Academia Nacional de Medicina, Buenos Aires, Argentina

Garcia-Chavez J.:
 Unidad Medica de Alta Especialidad, Centro Médico Nacional La Raza, Mexico City, Mexico

Moreno-Rodriguez B.:
 Servicio de Hematología, Hospital del Niño, Panama City, Panama

Rodrigues M.B.:
 Centro de Hemofilia, São Paulo, Brazil

 Hospital das Clinicas da Universidade de São Paulo (USP), São Paulo, Brazil

Rodriguez-Grecco I.:
 Centro Hospitalario Pereira Rossell, Hospital de Clinicas, Montevideo, Uruguay

Solano M.H.:
 Hospital de San Jose, Fundacion Universitaria de Ciencias de la Salud, Bogota, Colombia

Chumpitaz G.:
 Hospital Nacional Edgardo Rebagliati M., Lima, Peru

Morales-Gana M.M.:
 Hospital Roberto del Rio, Santiago, Chile

Ruiz-Sáez A.:
 Centro Nacional de Hemofilia, Banco Municipal de Sangre, Caracas, Venezuela
ISSN: 13518216
Editorial
WILEY-BLACKWELL, COMMERCE PLACE, 350 MAIN ST, MALDEN 02148, MA USA, Estados Unidos America
Tipo de documento: Article
Volumen: 20 Número: 1
Páginas: 63-70
WOS Id: 000328733300019
ID de PubMed: 24354487
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