Primary cutaneous blastic plasmacytoid dendritic cell neoplasm in a child: A challenging diagnosis and management
Por:
Rivas-Calderón M.K., Cheirif-Wolosky O., Rosas-Romero M.E., Toussaint-Caire S., Duran-McKinster C., González-Pedroza M.D.L., López-Santiago N.C., García-Romero M.T.
Publicada:
1 ene 2021
Resumen:
Blastic plasmacytoid dendritic cell neoplasm (BPDCN) is a rare and aggressive malignancy of the skin and hematopoietic system. There are few pediatric cases reported in the literature. Management of primary cutaneous BPDCN is challenging because, despite an apparently indolent clinical presentation, rapid dissemination with high mortality can occur. We describe a child with isolated cutaneous involvement who had a good response to chemotherapy as first-line treatment of BPDCN. © 2020 Wiley Periodicals LLC.
Filiaciones:
Rivas-Calderón M.K.:
Dermatology Department, National Institute of Pediatrics, Mexico City, Mexico
Cheirif-Wolosky O.:
Dermatology Department, National Institute of Pediatrics, Mexico City, Mexico
Rosas-Romero M.E.:
Dermatology Clinic, Medica Sur Hospital, Mexico City, Mexico
Toussaint-Caire S.:
Dermatopathology Department, Hospital General Dr. Manuel Gea González, Mexico City, Mexico
Duran-McKinster C.:
Dermatology Department, National Institute of Pediatrics, Mexico City, Mexico
González-Pedroza M.D.L.:
Hematology Department, National Institute of Pediatrics, Mexico City, Mexico
López-Santiago N.C.:
Hematology Department, National Institute of Pediatrics, Mexico City, Mexico
García-Romero M.T.:
Dermatology Department, National Institute of Pediatrics, Mexico City, Mexico
|