Transgenic GDNF Positively Influences Proliferation, Differentiation, Maturation and Survival of Motor Neurons Produced from Mouse Embryonic Stem Cells


Por: Cortes, Daniel, Robledo-Arratia, Yolanda, Hernandez-Martinez, Ricardo, Escobedo-Avila, Itzel, Bargas, Jose, Velasco, Ivan

Publicada: 12 sep 2016
Categoría: Cellular and Molecular Neuroscience

Resumen:
Embryonic stem cells (ESC) are pluripotent and thus can differentiate into every cell type present in the body. Directed differentiation into motor neurons (MNs) has been described for pluripotent cells. Although neurotrophic factors promote neuronal survival, their role in neuronal commitment is elusive. Here, we developed double-transgenic lines of mouse ESC (mESC) that constitutively produce glial cell line-derived neurotrophic factor (GDNF) and also contain a GFP reporter, driven by HB9, which is expressed only by postmitotic MNs. After lentiviral transduction, ESC lines integrated and expressed the human GDNF (hGDNF) gene without altering pluripotency markers before differentiation. Further, GDNF-ESC showed significantly higher spontaneous release of this neurotrophin to the medium, when compared to controls. To study MN induction, control and GDNF cell lines were grown as embryoid bodies and stimulated with retinoic acid and Sonic Hedgehog. In GDNF-overexpressing cells, a significant increase of proliferative Olig2+ precursors, which are specified as spinal MNs, was found. Accordingly, GDNF increases the yield of cells with the pan motor neuronal markers HB9, monitored by GFP expression, and Isl1. At terminal differentiation, almost all differentiated neurons express phenotypic markers of MNs in GDNF cultures, with lower proportions in control cells. To test if the effects of GDNF were present at early differentiation stages, exogenous recombinant hGDNF was added to control ESC, also resulting in enhanced MN differentiation. This effect was abolished by the co-addition of neutralizing anti-GDNF antibodies, strongly suggesting that differentiating ESC are responsive to GDNF. Using the HB9::GFP reporter, MNs were selected for electrophysiological recordings. MNs differentiated from GDNF-ESC, compared to control MNs, showed greater electrophysiological maturation, characterized by increased numbers of evoked action potentials (APs), as well as by the appearance of rebound APs, sag inward rectification, spike frequency adaptation and spontaneous synaptic potentials. Upon challenge with kainate, GDNF-overexpressing cells are more resistant to excitotoxicity than control MNs. Together these data indicate that GDNF promotes proliferation of MN-committed precursors, promotes neuronal differentiation, enhances maturation, and confers neuroprotection. GDNF-expressing ESC can be useful in studies of development and disease.

Filiaciones:
Cortes, Daniel:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

 Univ Nacl Autonoma Mexico, Lab Reprogramac Celular, Inst Fisiol Celular, Inst Nacl Neurol & Neurol Manuel Velasco Suarez, Mexico City, DF, Mexico

Robledo-Arratia, Yolanda:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

Hernandez-Martinez, Ricardo:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

Escobedo-Avila, Itzel:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

Bargas, Jose:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

Velasco, Ivan:
 Univ Nacl Autonoma Mexico, Inst Fisiol Celular Neurociencias, Mexico City, DF, Mexico

 Univ Nacl Autonoma Mexico, Lab Reprogramac Celular, Inst Fisiol Celular, Inst Nacl Neurol & Neurol Manuel Velasco Suarez, Mexico City, DF, Mexico
ISSN: 16625102
Editorial
FRONTIERS RESEARCH FOUNDATION, PO BOX 110, LAUSANNE, 1015, SWITZERLAND, Suiza
Tipo de documento: Article
Volumen: 10 Número: SEP2016
Páginas:
WOS Id: 000383174400001
ID de PubMed: 27672361