Mandibular distraction osteogenesis in a patient with Melnick-Needles syndrome
Por:
Molina, FM, Morales, C, Taylor, JA
Publicada:
1 ene 2008
Resumen:
Melnick Needles syndrome is an X-inked-dominant skeletal dysplasia in which there is deficient osteoblastic activity. Patients present with craniofacial anomalies consisting of a prominent forehead, exorbitism, mandibular hypoplaisia, cheek fullness, and class II malocclusion. Severe mandibular hypoplasia leads to upper airway restriction, an increased incidence of sleep, apnea and pneumonias, and occasionally respiratory failure. This is a report of a patient with Melnick-Needles syndrome who presented to our unit after multiple bouts of respiratory failure and with a tracheostomy in whom mandibular distraction osteogenesis was used to retire her tracheostomy and to cure her sleep apnea. The patient underwent bilateral, external, unidirectional mandibular distraction with a vector parallel to the occlusal plane. After a latency period of 5 days, distraction was initiated at a rate of I mm/day for 34 days. At this point, the patient was able to breathe with the tracheostomy plugged, an
Filiaciones:
Molina, FM:
Univ Nacl Autonoma Mexico, Hosp Gen Dr Manuel Gea Gonzalez, Postgrad Div Med Sch, Dept Plast & Reconstruct Surg, Mexico City 04510, DF, Mexico
Morales, C:
Univ Nacl Autonoma Mexico, Hosp Gen Dr Manuel Gea Gonzalez, Postgrad Div Med Sch, Dept Plast & Reconstruct Surg, Mexico City 04510, DF, Mexico
Taylor, JA:
Univ Nacl Autonoma Mexico, Hosp Gen Dr Manuel Gea Gonzalez, Postgrad Div Med Sch, Dept Plast & Reconstruct Surg, Mexico City 04510, DF, Mexico
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